Yes, they changed EHK mostly because it had too many names. In some countries it was bCIE or autosomal dominant ichthyosis. In others, it was EHK, EI, or some other combination of acronyms.
They changed Lamellar and CIE (nbCIE) to ARCI, too. It happened about 2 years ago, but new journal articles and literature really just started to show up with the new designations in the last year.
Ichthyosis-en-Confetti Type 2
Husband, Nathan - 10, Elliot - 7, Oliver - 4, all affected.
I also have an unaffected daughter, age 8.
email: jennifer at confettiskin dot com
facebook - find me on "ichthyosis mommy spot" or "friends of ichthyosis"