XLI runs in families and can be tested for prenatally, unlike LI that appears out of a completely unaffected family.
Kiwi, My kids don't have your type, so I'm not much use, but there's a poster here called threerxli that has many posts with very helpful info. Do a search for her.
Ichthyosis-en-Confetti Type 2
Husband, Nathan - 10, Elliot - 7, Oliver - 4, all affected.
I also have an unaffected daughter, age 8.
email: jennifer at confettiskin dot com
facebook - find me on "ichthyosis mommy spot" or "friends of ichthyosis"